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October 24th, 2013
Carrousel du Louvre, Paris
Unexpected guests in pulmonary arterial hypertension
Marc HUMBERT
Bicêtre Le Plessis Robinson
⤢
PAH: A SEVERE PULMONARY VASCULAR DISEASE
A RARE BUT NOT AN ORPHAN DISEASE
FROM ENDOTHELIAL CELL DYSFUNCTION TO INNOVATIVE THERAPIES
UNMET NEED IN THE MODERN MANAGEMENT ERA
THE FRENCH CENTRE FOR PAH RESEARCH, EDUCATION AND CARE
AIM 1 : INNOVATIVE PAH BIOMARKERS
ELECTRONIC NOSE: PROMISING EMERGING TECHNOLOGY
ELECTRONIC NOSE: PROOF OF CONCEPT IN PAH
AIM 2: NOVEL TARGETS IN PAH
A GROUNDBREAKING DISCOVERY INFLAMMATION, AN UNEXPECTED TARGET IN PAH
THINK DIFFERENT
LINKING ENDOTHELIAL DYSFUNCTION AND INFLAMMATION (MIF/ CD74 PATHWAY)
ACTIVATION OF CD74 WITH MIF LEADS TO A PROINFLAMMATORY ENDOTHELIAL CELL PHENOTYPE
PROOF OF CONCEPT: INHIBITION OF THE MIF/CD74 PATHWAY IN EXPERIMENTAL PH
FUTURE DIRECTIONS
ACKNOWLEDGEMENTS
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